Scheuermann's disease
Scheuermann's disease (pronounced 'Shoy-eh-ah-
man' though very often mispronounced as
'Sherman') is a self-limiting skeletal disorder
of childhood. It is also known as Sherman's
Disease, Scheuermann's kyphosis (since it results
in kyphosis), Calvé disease and Juvenile
Osteochondrosis of the Spine. It is named after
Holger Werfel Scheuermann. Scheuermann's
disease describes a condition where the vertebrae
grow unevenly with respect to the Sagittal plane;
that is, the anterior angle is often greater than
the posterior. This uneven growth results the
signature "wedging" shape of the vertebrae,
causing kyphosis.
Scheuermann's disease is considered to be a a
form of juvenile osteochondrosis of the spine. It
is found mostly in teenagers and presents a
significantly worse deformity than postural
kyphosis. Patients suffering with Scheuermann's
kyphosis cannot consciously correct their
posture. The apex of their curve, located in the
thoracic vertebrae, is quite rigid.

The seventh and tenth thoracic vertebrae are most
commonly affected. It causes backache and spinal
curvature. In very serious cases it may cause
internal problems and spinal cord damage, but
these cases are extremely rare. The curvature of
the back decreases height, thus putting pressure
on internal organs, wearing them out more quickly
than the natural aging process; surgical
procedures are almost always recommended in this
case.
Comorbid Conditions
Many with Scheuermann's disease often have an
excessive lordotic curve in the lumbar spine;
this is the body's natural way to compensate for
the kyphotic curve above. Interesting, many with
Scheuermann's disease have very large lung
capacities and males often have broad, barrel
chests. Most people have FVC scores above
average. It has been proposed that this is the
body's natural way to compensate for a loss of
breathing depth.
Often patients have tight hamstrings, which,
again, is related to the body compensating for
excessive spinal curative, though this is also
debated (for example, some suggest the tightness
of ligament is the initial cause of the growth
abnormality). In addition to the common lordosis,
it has been suggested that between 20-30% of
patients with Scheuermann's Disease also have
scoliosis, though most cases are negligible. In
more serious cases, however, the combination is
classified as a separate condition known as
kyphoscoliosis.
Successfully corrected
Scheuermann's disease can be successfully
corrected with surgical procedures, almost all of
which include spinal fusion and hardware
instrumentation, i.e., rods, pedicle screws, etc.
While many patients are typically interested in
getting surgery for their correction, it is
important to realize the surgery aims to reduce
pain, and not cosmetic defect. As always,
surgical intervention should be used as a last
resort once conservative treatment fails or the
patient's health is in imminent danger as any
surgical procedure is not without risk; however,
the chances of complication are relatively low
and the surgeries are often successful.
One of the largest debates surrounding
Scheuermann's disease correction is the use of
very different correction procedures. There are
different techniques to correct kyphosis; usually
the differences being posterior/anterior entry or
posterior entry (rear) only. The classic surgical
procedure partially entails entering two titanium
rods, each roughly one and a half feet long, into
the back on either side of the spine. Eight
titanium screws and hardware are drilled through
the bone and secures them in place onto either
side of the spine. On the internal-facing side of
the spine, ligaments (which can be too short,
pulling the spine into the general shape of
kyphosis) must be surgically cut or released, not
only stopping part of the cause of the kyphosis,
but also allowing the titanium rods to pull the
spine into a more natural position. Normally, the
damaged discs between the troubled vertebrae
(wedged vertebrae) are removed and replaced with
cartilage from the hip or other parts of the
vertebrae, which once healed or 'fused' will
solidify. The titanium instrumentation holds
everything in place during healing and is not
necessary once fusion completes. Recovery begins
in the hospital and depending on whether the
operation is one or two stage the patient can
expect to be in hospital for minimum of a week
possibly longer depending on recovery. They will
then often be required to wear a brace for
several months to ensure the spine heals
correctly leaving the patient with the correct
posture. The titanium instrumentation can stay in
the body permanently, or be removed years later.
Patients undergoing surgery for Scheuermann's
disease often need physical therapy to manage
pain and mobility, however their range of motion
is generally not limited very much. Recovery from
kyphosis correction surgery can be very long;
typically patients are not allowed to lift
anything above 5 of 10 pounds for 6 months to a
year. Many are out of work for at least 6 months.
However, once the fusion is solidified, most
patients can return to their usual lifestyle with
one to two years.
Advisable not to carry mattresses, especially up
stairs due to the increased strain on the
ligamentum flavum predisposing to discopathy.
Complications Spinal fusion for kyphosis and
scoliosis is extremely invasive surgery. The risk
of undergoing spinal fusion surgery for kyphosis,
like in scoliosis is estimated to be 5 % .
Possible complications may be inflammation of the
soft tissue or deep inflammatory processes,
breathing impairments, bleeding and nerve
injuries. However, according to the latest
evidence the rate of complications is beyond that
rate. As early as five years after surgery
another 5% require reoperation and today it is
not yet clear what to expect from spine surgery
in the long-term. Taking into account
that signs and symptoms of spinal deformity
cannot be changed by surgical intervention,
surgery remains to be a cosmetic indication.
Unfortunately the cosmetic effects of
surgery are not necessarily stable.] In case
one decides to undergo surgery a specialized
centre should be preferred.
External links:
http://orthoinfo.aaos.org/fact/thr_report.cfm?
Thread_ID=247&topcategory=Spine
http://www.back.com/causes-developmental-
scheuermann.html
http://www.emedicine.com/pmr/topic129.htm]
Scheuermann's Kyphosis (Scheuermann's Disease):
Abnormal Curvature of the Spine
http://www.allaboutbackandneckpain.com/html/spine
sub.asp?id=27


